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Table 2 Median age and range at diagnosis of Lynch syndrome associated cancer

From: Cancer risk in MLH1, MSH2 and MSH6 mutation carriers; different risk profiles may influence clinical management

 

MLH1

MSH2

MSH6

Colorectal cancer

47 (25-79)

44 (20-82)

53 (32-84)

Endometrial cancer

51 (46-54)

46 (36-55)

56 (47-67)

Ovarian carcinoma

52 (52-52)

47 (45-48)

49 (35-51)

Small bowel cancer

54 (54-54)

36 (23-49)

-

Transitional cell carcinoma

-

58 (32-59)

-