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Table 2 Risk of neoplastic disease manifestation in individual organs in cases of hamartomatous polyposis syndromes

From: Hamartomatous polyposis syndromes

Organ Cumulative risk (%) of cancer development in individual syndromes of hamartomatous polyposis
Juvenile polyposis syndrome Peutz - Jeghers` syndrome PHTS
Thyroid gland    3-10
Breasts   (8% risk by age 40, 45% by age 70). 25-50
Stomach 21 29  
Pancreas Two cases 36  
Small intestine   13  
Large bowel 9%-68% (17%-22% by age 25 57 (9% ba age 40)  
Kidneys    2
Urinary bladder    3
Uterus   9 6
Uterine cervix   10 3
Ovaries   21 2
Testes   9